A Case Of Limbal Dermoid

We are reporting a case of a newborn with a severe presentation of limbal dermoid with a presentation typical of Goldenhar syndrome, where we followed for almost 5 months now since birth and we are unable to do any surgical intervention due to the severity of the presentation and the depth of corneal involvement together with the challange of other comorbidities in the child

we reported the case by taking photos of the lesions after permisiion of the parents and the child is followed up now for 5 months. Reviewing the literature for similar cases and current surgical options for treatment was done and till now thw decision was difficult to take . This made this case a challanging case.

1 d Old male
Full Term, Vaginal Delivery
IOP: 8 mmHg 8 mmHg
Eyelids:
No Coloboma OU
Ant Seg:
OD 2 whitish masses elevated and spherical encroaching on the limbus both nasally and temporally but the nasal one is larger and encroaching on 1/3 of the pupil and even after mid dilatation detection of the red reflex was difficult
OS one whitish mass elevated and spherical encroaching on the limbus and temporally but encroaching only on <1/4 of the pupil and after mid dilatation detection of the red reflex was possible
Both eyes were difficult to fully dilate after tropicamide instillation
Dilated Fundus Exam:
OD Fundus was difficult to detect
OS can be seen with normal disk with multiple scattered retinal hges mostly due to vaginal delivery

Limbal dermoids associated with Goldenhar Syndrome, although reported in the literature, can sometimes be severe and challenging to the degree of being a really difficult decision and consideration of the child's condition and involving the parents in every step is really important