Microsoherophakia: Case Report Of Cataract Extraction Of Young Woman Diagnosed With Microspherophakia And Secondary Glaucoma First Time Diagnosed In Gyumri Medical Center

With this abstract I want to present a case of bilateral microspherophakia, with varied clinical presentations.. To
show how we treated this patients and tell the results.

Microspherophakia is a rare congenital entity that is characterized by a bi-convex spherical lens with reduced equatorial
diameter. This is primarily because of the developmental anomaly of zonules. The clinical manifestations can range from
asymptomatic to high lenticular myopia, acute angle-closure, or chronic glaucoma. Microspherophakia is often a bilateral
condition.

Gyumri Medical Center Ophthalmology Service, Gyumri, Armenia

We present a case of microspherophakia, presenting as lens subluxation and secondary glaucoma.
A 44-year-old young woman presented to the ophthalmology service, with drop of visual acuity in her both eyes and pain
in the eyes
The Patient was complaining of very low vision, that started from childhood and got worse over years
Her BCVA OU- 20/2000, IOP-37(Goldman)
Her past medical history was unremarkable, she takes no medications and eye drops
Eye examination - clear cornea, anterior chamber shallow in superior part, and with normal depth in inferior part.
With dilated pupil examination( poor dilation)- lens subluxation, absence of 80% of zonules (superior, temporal, nasal)
and no clear view of fundus.
WTW- 9.8 mm
Patient diagnosed: OU- High Myopia, Myopic Astigmatism, Cataract (nuclear sclerosis 3+), Lens Subluxation,
Microspherophakia, Secondary Glaucoma
IOL calculation was done with SRK-II formula, and we used monofocal hydrophobic IOL, because of local problems with
toric IOL
Patient underwent OS- Cataract phacoemulsification and IOL Iris fixation ( A. Hovsepyan method)
OD- Intracapsular cataract extraction and IOL Iris fixation (A. Hovsepyan method)
Both surgeries went without intraoperatve complications, without vitreous loss.
Postop
BCVA OD-20/40 , IOP 17
BCVA OS- 20/60, IOP 19
Patient has postop Myopic Astigmatis

Now Patient is under observation.

Microspherophakia is a rare, but potentially blinding disease with a variety of associated systemic syndromes and varied
clinical presentations. Early identification of the disease, timely visual rehabilitation, and appropriate management of the
lens and glaucoma can help us prevent blindness from this condition. Multidisciplinary care with lifelong follow-up is
recommended.