Bilateral Intraorbital Cystic Lymphangioma : About A Case

Clinical and radiological description of complicated bilateral intraorbital cystic lymphangioma in an infant

Lymphangioma is a benign tumor with progressive development. Orbital localization is rare (1 to 2% of orbital tumors), but serious by its functional and aesthetic impact often important, as well as by its difficult and often incomplete surgical excision.

This is a one-month-old infant without significant pathological ATCD, admitted for a lower bilateral orbital swelling and painless more marked left.
The patient received ophthalmological examination and additional radiological examinations

  The ophthalmological examination finds in the right eye a clouded microcornea and microphthalmia, and the examination of the left eye is inaccessible.

ultrasound: At the level of the right eye: globe decreased in size, globose and echogenous appearance of the lens, transonic vitreous, appearance of coloboma of the posterior pole 
The left eye: enlarged and elongated appearance of the posterior segment with posterior coloboma, examination of the anterior segment not analyzable.

orbito-cerebral MRI : A bilateral intraorbital cystic formation of 23 * 15 * 24mm on the left and 19 * 12 * 16 on the right evoking first a bilateral cystic lymphangioma intraorbital deforming the two eyeballs with hypoplasia of the optic nerves.

Given its often infiltrating character on the local and locoregional level with sometimes a major functional and aesthetic impact, the prognosis of orbital lymphangiomas remains generally reserved