Strange Cataract In Young Patient With Multiple Exostosing Disease
Published 2023 - 41st Congress of the ESCRS
Reference: PO0065 | Type: Case report | DOI: 10.82333/n8j0-h875
Authors: Paula Alonso Barreiros* 1 , CARLOS LLORENTE LA ORDEN 1 , YOLANDA POZA MORALES 1 , CRISTINA VIDAL ARRANZ 1 , ESTHER MATA DIAZ 1 , CARLOS DE PABLO MARTIN 1
1HOSPITAL CENTRAL DE LA CRUZ ROJA SAN JOSE Y SANTA ADELA,MADRID,Spain
TO DESCRIBE A CASE OF ANTERIOR CAPSULAR FIBROSIS IN A 24-YEAR-OLD PATIENT WITH MULTIPLE EXOSTOSING DISEASE
DESCRIPTIVE CASE
A 24-YEAR-OLD PATIENT WHO VISITED OUR SERVICE DUE TO DECREASED VISUAL ACUITY IN THE LEFT EYE. AS A PERSONAL HISTORY, THE PATIENT PRESENTED A MULTIPLE EXOSTOSING DISEASE THAT HAS REQUIRED MULTIPLE SURGERIES FOR THE REMOVAL OF OSTEOCONDROMAS
THE PATIENT PRESENTED A VISUAL ACUITY OF 20/25 IN THE RIGHT EYE AND OF 20/60 IN THE LEFT EYE, CORNEAL FERRIC DEPOSIT IN BOTHE EYES, TRANSPARENT CRYSTALLINEON RIGHT EYE AND CATARACT WITH A LARGE FIBROSIS OF THE ANTERIOR CAPSULE THAT PREVENTED VISUALIZING THE FUNDUS ON LEFT EYE . BOTH EYES PRESENTED A CYLINDER OF -6 DIOPTERS, FOR WHICH A PENTACAM AND A MEASUREMENT OF CORNEAL HYSTERESIS WERE PERFORMED, RULED OUT ECTASIA
AFTER CATARACT SURGERY WITH TORIC LENS IMPLANT THE PATIENT PRESENTS A VA IN LE OF 20/32
HEPARAN SULFATE IS INVOLVED IN THE BONE SYSTEM AND THERE ARE CASES DESCRIBED THAT ASSOCIATE CORNEAL ALTERATIONS, SUCH AS KERATOCONUS AND COULD BE INVOLVED IN THE FIBROSIS OF THE ANTERIOR CAPSULE IN THIS CASE