ESCRS - PO1005 - Treatment Of Glaucoma In Children Associated With Sturge Weber Syndrome With Glaucoma Drainage Devices

Treatment Of Glaucoma In Children Associated With Sturge Weber Syndrome With Glaucoma Drainage Devices

Published 2025 - 43rd Congress of the ESCRS

Reference: PO1005 | Type: Poster | DOI: 10.82333/84r5-th50

Authors: Ana Barbara Marinčič* 1 , Vladimir Pfeifer 1 , Manca Tekavčič Pompe 1

1Eye hospital Ljubljana,University medical center Ljubljana,Ljubljana,Slovenia

Purpose

The purpose of this case series is to present the usefulness of glaucoma drainage devices (GDD) implantation in the treatment of glaucoma associated with Sturge-Weber syndrome.

Setting

We present four consecutive cases of children (girls aged from 2.5 to 16 years) with glaucoma associated with SWS who were treated with the implantation of a glaucoma drainage device (Baerveldt, BGV, or Ahmed, AGV) in the period 2013–2025. On average, the children underwent surgery at the age of 9.5 years, with a mean follow-up duration of 48 months.

Methods

Case 1: A 16-year-old girl had a BGV implanted in her left eye at 12, with a 45-month follow-up. A revision was needed six months later. Visual acuity remains 0.2–0.3, C/D = 0.5–0.6, and IOP is stable without therapy.

Case 2: A 15-year-old girl had an AGV implanted at 9, with a 72-month follow-up. A valve revision was done after five years. IOP is controlled with topical therapy; C/D = 0.5, visual acuity 1.2 s.c.

Case 3: A 2.5-year-old girl had an AGV implanted at two months, with a 28-month follow-up. IOP remains normal withtopical therapy.

Case 4: A 13-year-old girl had a BGV implanted at 1.5 years, with a 12-year follow-up. After cataract surgery and IOL repositioning, IOP is stable, and no glaucomatous progression is noted.

Results

In two patients, GDD implantation alone was sufficient to control IOP, while in two cases, additional antiglaucoma therapy was required for IOP regulation. The glaucomatous defect remained stable in all cases.

Conclusions

The treatment of glaucoma in children with SWS using GDD implantation is an effective method supported by the literature.